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Last updated: 26-Jun-98
REFERENCE FORMAT: Author Lastname; Firstname; Article Number; Article Title; Journal or Book; Year; Volume; Page Numbers
Asano ; K. ; 220* ; Changes in the rat liver mitochondrial DNA upon aging ; Mech Ageing Dev ; 1991 ; 60(3) ; 275-84
Bakker ; HD ; 3162 ; Depletion of mitochondrial deoxyribonucleic acid in a family with fatal neonatal liver disease ; J Pediatr ; 1996 ; 128(5) ; 683-687
Bioulac-Sage ; P ; 847 ; Fatal neonatal liver failure and mitochondrial cytopathy (oxidative phosphorylation deficiency): a light and electron microscopic study of the liver. ; Hepatology ; 1993 ; 18(4) ; 839-46
Boles ; RG ; 2337* ; Biochemical diagnosis of fatty acid oxidation disorders by metabolite analysis of postmortem liver [see comments]. ; Human Pathology ; 1994 ; 25(8) ; 735-41
Britton ; CH ; 3246* ; Human liver mitochondrial carnitine palmitoyltransferase I: characterization of its cDNA and chromosomal localization and partial analysis of the gene. ; Proc Natl Acad Sci USA ; 1995 ; 92(6) ; 1984-1988
Broide ; E ; 5741 ; Type IV 3-methylglutaconic (3-MGC) aciduria: a new case presenting with hepatic dysfunction. ; Pediatr Neurol ; 1997 ; 17(4) ; 353-5
Bucheler ; K ; 394 ; Localization of the ATP/ADP translocator in the inner membrane and regulation of contact sites between mitochondrial envelope membranes by ADP. A study on freeze-fractured isolated liver mitochondria. ; Biochim Biophys Acta ; 1991 ; 1056(3) ; 233-42
Chabrol ; B ; 1473* ; Valproate-induced hepatic failure in a case of cytochrome c oxidase deficiency [see comments]. ; European Journal of Pediatrics ; 1994 ; 153(2) ; 133-5
Coppel ; RL ; 3313 ; Primary biliary cirrhosis: the molecule and the mimic. ; Immunol Rev ; 1995 ; 144 ; 17-49
de Vries ; DD ; 2226 ; Detection of extremely low levels of wild-type mitochondrial DNA in the liver of a patient with Pearson syndrome by a sensitive PCR assay. ; Journal of Inherited Metabolic Disease ; 1992 ; 15(3) ; 307-10
Duran ; M ; 2379 ; Diagnosis of medium-chain acyl-CoA dehydrogenase deficiency in lymphocytes and liver by a gas chromatographic method: the effect of oral riboflavin supplementation. ; Pediatric Research ; 1992 ; 31(1) ; 39-42
Eaton ; S ; 2829 ; Investigation of beta-oxidation in human liver biopsies. ; Clin Chim Acta ; 1993 ; 220(2) ; 219-24
Eaton ; S ; 3381 ; beta-Oxidation in human alcoholic and non-alcoholic hepatic steatosis. ; Clin Sci ; 1996 ; 90(4) ; 307-313
Eaton ; S ; 3382 ; Mitochondrial beta-oxidation in human alcoholic liver disease. ; Biochem Soc Trans ; 1995 ; 23(3) ; 497S
Edery ; P ; 1472* ; Liver cytochrome c oxidase deficiency in a case of neonatal-onset hepatic failure. ; European Journal of Pediatrics ; 1994 ; 153(3) ; 190-4
Ehara ; H ; 5837 ; New autosomal-recessive syndrome of Leber congenital amaurosis, short stature, growth hormone insufficiency, mental retardation, hepatic dysfunction, and metabolic acidosis. ; Am J Med Genet ; 1997 ; 71(3) ; 258-66
Espeel ; M ; 5841 ; Biogenesis of peroxisomes in fetal liver. ; Microsc Res Tech ; 1997 ; 39(5) ; 453-66
Fayon ; M ; 853 ; Fatal neonatal liver failure and mitochondrial cytopathy: an observation with antenatal ascites. ; Gastroenterology ; 1992 ; 103(4) ; 1332-5
Fellman ; V ; 5844 ; Iron-overload disease in infants involving fetal growth retardation, lactic acidosis, liver haemosiderosis, and aminoaciduria. ; Lancet ; 1998 ; 351(9101) ; 490-3
Fukushima ; S ; 3434 ; The frequency of 4977 base pair deletion of mitochondrial DNA in various types of liver disease and in normal liver. ; Hepatology ; 1995 ; 21(6) ; 1547-1551
Gershwin ; ME ; 3448* ; New knowledge in primary biliary cirrhosis. ; Hosp Pract (Off Ed) ; 1995 ; 30(8) ; 29-36
Goncalves ; I ; 3456* ; Mitochondrial respiratory chain defect: a new etiology for neonatal cholestasis and early liver insufficiency. ; J Hepatol ; 1995 ; 23(3) ; 290-294
Guillaume ; MP ; 3479* ; Subacute mitochondrial liver disease in a patient with AIDS: possible relationship to prolonged fluconazole administration. ; Am J Gastroenterol ; 1996 ; 91(1) ; 165-168
Harding ; BN ; 1993* ; Progressive neuronal degeneration of childhood with liver disease (Alpers' disease) presenting in young adults. [Review] ; Journal of Neurology, Neurosurgery & Psychiatry ; 1995 ; 58(3) ; 320-5
Hertz ; R ; 5916 ; Fatty acyl-CoA thioesters are ligands of hepatic nuclear factor-4alpha. ; Nature ; 1998 ; 392(6675) ; 512-6
Hirawake ; H ; 2854 ; Human complex II (succinate-ubiquinone oxidoreductase): cDNA cloning of the flavoprotein (Fp) subunit of liver mitochondria. ; J Biochem (Tokyo) ; 1994 ; 116(1) ; 221-7
Hou ; JW ; 3535* ; Metabolic function and liver histopathology in Reye-like illnesses. ; Acta Paediatr ; 1996 ; 85(9) ; 1053-1057
Ikai ; I ; 454 ; Rate of ATP synthesis in the perfused rat liver by 31P cryo-NMR. ; J Biol Chem ; 1990 ; 265 ; 22097-100
Isaacs Jr ; JD ; 5939 ; Maternal acute fatty liver of pregnancy associated with fetal trifunctional protein deficiency: molecular characterization of a novel maternal mutant allele. ; Pediatr Res ; 1996 ; 40(3) ; 393-8
Ishii ; K ; 5942 ; Two survival cases of alcoholic lactic acidosis complicated with diabetes mellitus and alcoholic liver disease. ; Alcohol Clin Exp Res ; 1996 ; 20(9 Suppl) ; 387A-390A
Jeevaratnam ; K ; 493 ; In vitro and in vivo effect of methyl isocyanate on rat liver mitochondrial respiration. ; Toxicol Appl Pharmacol ; 1992 ; 117(2) ; 172-9
Kita ; K ; 2688 ; Human complex II (succinate-ubiquinone oxidoreductase): cDNA cloning of iron sulfur (Ip) subunit of liver mitochondria. ; Biochem Biophys Res Commun ; 1990 ; 166(1) ; 101-8
Kokawa ; N ; 5994 ; Pregnancy and delivery complicated by mitochondrial myopathy, encephalopathy, lactic acidosis, and stroke-like episodes. ; Obstet Gynecol ; 1998 ; 91(5 Pt 2) ; 865
Le Bras ; P ; 921* ; Metabolic, hepatic and muscular changes during zidovudine therapy: a drug-induced mitochondrial disease? [letter]. ; AIDS ; 1994 ; 8(5) ; 716-7
Leung ; PS ; 3696* ; Molecular aspects and the pathological basis of primary biliary cirrhosis. ; J Autoimmun ; 1996 ; 9(2) ; 119-128
Liverini ; G ; 400 ; The effect of cold exposure on rat liver mitochondrial respiratory capacity. ; Comp Biochem Physiol [B] ; 1991 ; 98(4) ; 583-5
Maaswinkel-Mooij ; PD ; 3730 ; Depletion of mitochondrial DNA in the liver of a patient with lactic acidemia and hypoketotic hypoglycemia ; J Pediatr ; 1996 ; 128(5) ; 679-683
Mahler ; H ; 6035 ; Fulminant liver failure in association with the emetic toxin of Bacillus cereus [see comments] ; N Engl J Med ; 1997 ; 336(16) ; 1142-8
Mazzella ; M ; 6063 ; Severe complex I deficiency in a case of neonatal-onset lactic acidosis and fatal liver failure. ; Acta Paediatr ; 1997 ; 86(3) ; 326-9
Mazziotta ; MR ; 797 ; Fatal infantile liver failure associated with mitochondrial DNA depletion. ; Journal of Pediatrics ; 1992 ; 121(6) ; 896-901
McKenzie ; R ; 872* ; Hepatic failure and lactic acidosis due to fialuridine (FIAU), an investigational nucleoside analogue for chronic hepatitis B [see comments]. ; New England Journal of Medicine ; 1995 ; 333(17) ; 1099-105
Mehrotra ; S ; 402 ; Influence of some biological response modifiers on swelling of rat liver mitochondria in vitro. ; Mol Cell Biochem ; 1993 ; 124(2) ; 101-6
Mela ; L. ; 533 ; Defective oxidative metabolism of rat liver mitochondria in hermorrhagic and endotoxin shock ; Am J Physiol ; 1971 ; 220 ; 571-
Muller-Hocker ; J ; 6106 ; Defects of the respiratory chain in the normal human liver and in cirrhosis during aging. ; Hepatology ; 1997 ; 26(3) ; 709-19
Murphy ; MG ; 6110 ; Sequestration of coenzyme A by the industrial surfactant, Toximul MP8. A possible role in the inhibition of fatty-acid beta-oxidation in a surfactant/influenza B virus mouse model for acute hepatic encephalopathy. ; Biochim Biophys Acta ; 1997 ; 1361(1) ; 103-13
Narkewicz ; MR ; 2004 ; Liver involvement in Alpers disease. ; Journal of Pediatrics ; 1991 ; 119(2) ; 260-7
Pandha ; HS ; 969 ; Treating acidosis in fulminant hepatic failure: the case against use of bicarbonate solutions [letter; comment]. ; New Zealand Medical Journal ; 1992 ; 105(937) ; 271
Pearce ; RE ; 3933* ; Effects of freezing, thawing, and storing human liver microsomes on cytochrome P450 activity. ; Arch Biochem Biophys ; 1996 ; 331(2) ; 145-169
Pepper ; GM ; 6156 ; Lactic acidosis associated with Glucophage use in a man with normal renal and hepatic function [letter] ; Diabetes Care ; 1997 ; 20(2) ; 232-3
Perper ; JA ; 2368 ; Fatty liver, encephalopathy, and sudden unexpected death in early childhood due to medium-chain acyl-coenzyme A dehydrogenase deficiency. ; American Journal of Forensic Medicine & Pathology ; 1992 ; 13(4) ; 329-34
Peterson ; KL ; 6161 ; Functional role of a distal (3'-phosphate) group of CoA in the recombinant human liver medium-chain acyl-CoA dehydrogenase-catalysed reaction. ; Biochem J ; 1997 ; 325 ( Pt 3) ; 751-60
Quentin ; E ; 364* ; Temperature dependence of the coupling efficiency of rat liver oxidative phosphorylation: role of adenine nucleotide translocator ; Biochem Biophys Res Commun ; 1994 ; 202(2) ; 816-21
Ramana ; KV ; 3976 ; Induction of hepatic cytochrome P450 by phenobarbitone in rhesus monkey (Macaca mulatta). ; Drug Chem Toxicol ; 1996 ; 19(1-2) ; 97-107
Romero ; R ; 6188 ; The difficulty with rapid communication: fulminant hepatic failure in infancy [editorial; comment] ; J Pediatr Gastroenterol Nutr ; 1998 ; 26(4) ; 472-4
Rosaeg ; OP ; 3999 ; Anaesthetic management of labour and delivery in the parturient with mitochondrial myopathy. ; Can J Anaesth ; 1996 ; 43(4) ; 403-407
Schafer ; DF ; 6210 ; Power failure, liver failure [editorial; comment] ; N Engl J Med ; 1997 ; 336(16) ; 1173-4
Schneider ; M ; 4049* ; Fatal hepatic necrosis following cardiac surgery and enflurane anaesthesia. ; Anaesth Intensive Care ; 1995 ; 23(2) ; 225-227
Scholmerich ; J ; 3100 ; Disturbed cellular energy metabolism in burns. Studies of rat liver ; Acta Biol Med Ger ; 1980 ; 39(10) ; 1051-1072
Schumer ; W. ; 534 ; Effect of endotoxemia on liver cell mitochondria in man ; Ann Surg ; 1970 ; 171 ; 875-
Shangraw ; RE ; 4068* ; Pharmacokinetics of dichloroacetate in patients undergoing liver transplantation. ; Anesthesiology ; 1996 ; 84(4) ; 851-858
Shinozawa ; S. ; 243* ; Effect of Aclarubicin and Doxorubicin on Rat Liver Mitochondrial Oxidative Phosphorylation ; Physiol Chem Phys Med NMR ; 1991 ; 23(2) ; 101-6
Sims ; HF ; 612 ; The molecular basis of pediatric long chain 3-hydroxyacyl-CoA dehydrogenase deficiency associated with maternal acute fatty liver of pregnancy. ; Proc Natl Acad Sci USA ; 1995 ; 92(3) ; 841-5
Smith ; JL ; 6253 ; Effect of exogenous cholesterol and dithiothreitol on the activity of human liver microsomal acyl-coenzyme A:cholesterol acyltransferase (ACAT). ; Clin Chim Acta ; 1996 ; 256(1) ; 13-25
Sokol ; RJ ; 2845 ; Oxidant injury to hepatic mitochondria in patients with Wilson's disease and Bedlington terriers with copper toxicosis. ; Gastroenterology ; 1994 ; 107(6) ; 1788-98
Soliman ; MS ; 6257 ; Evidence against peroxisome proliferation-induced hepatic oxidative damage. ; Biochem Pharmacol ; 1997 ; 53(9) ; 1369-74
Sottocasa ; G.L. ; 554 ; An electron-transport system associated with the outer membrane of liver mitochondria ; J Cell Biol ; 1967 ; 32 ; 415-39
Stephan ; JL ; 4119* ; Fulminant liver failure in a 12-year-old girl with sickle cell anaemia: favourable outcome after exchange transfusions. ; Eur J Pediatr ; 1995 ; 154(6) ; 469-471
Strunin ; L ; 4126* ; Hepatic necrosis after cardiac surgery ; Anaesth Intensive Care ; 1995 ; 23(6) ; 755-756
Sugden ; MC ; 4128 ; Regulation of hepatic pyruvate dehydrogenase kinase by insulin and dietary manipulation in vivo. Studies with the euglycaemic- hyperinsulinaemic clamp. ; Biochim Biophys Acta ; 1996 ; 1316(2) ; 114-120
Sugiyama ; S ; 2807 ; Changes in skeletal muscle, heart and liver mitochondrial electron transport activities in rats and dogs of various ages. ; Biochem Mol Biol Int ; 1993 ; 30(5) ; 937-44
Sustry ; P.S. ; 544 ; Distribution of coenzyme Q in rat liver cell fractions ; Nature ; 1961 ; 189 ; 577-
Taylor ; RW ; 1790* ; The control of mitochondrial oxidations by complex III in rat muscle and liver mitochondria. Implications for our understanding of mitochondrial cytopathies in man. ; Journal of Biological Chemistry ; 1994 ; 269(5) ; 3523-8
Thomson ; M ; 6322 ; Generalised mitochondrial cytopathy is an absolute contraindication to orthotopic liver transplant in childhood [see comments] ; J Pediatr Gastroenterol Nutr ; 1998 ; 26(4) ; 478-81
Triggs ; WJ ; 6326 ; Valproate-associated carnitine deficiency and malignant cerebral edema in the absence of hepatic failure. ; Int J Clin Pharmacol Ther ; 1997 ; 35(9) ; 353-6
Trost ; LC ; 6328 ; The mitochondrial permeability transition: a new pathophysiological mechanism for Reye's syndrome and toxic liver injury. ; J Pharmacol Exp Ther ; 1996 ; 278(3) ; 1000-5
Van Erven ; P.M.M. ; 551 ; Subacute necrotizing encephalomyelopathy (Leigh syndrome) associated with disturbed oxidation of pyruvate, malate and 2-oxoglutarate in muscle and liver ; Acta Neurologica Scandinavica ; 1985 ; 72 ; 36-42
Vancutsem ; PM ; 4215 ; In vitro and in vivo study of the effects of enrofloxacin on hepatic cytochrome P-450. Potential for drug interactions. ; Vet Hum Toxicol ; 1996 ; 38(4) ; 254-259
Varga ; J ; 713 ; Myopathy with mitochondrial alterations in patients with primary biliary cirrhosis and antimitochondrial antibodies. ; Arthritis & Rheumatism ; 1993 ; 36(10) ; 1468-75
Vilaseca ; MA ; 1005 ; Fatal hepatic failure with lactic acidaemia, Fanconi syndrome and defective activity of succinate:cytochrome c reductase. ; Journal of Inherited Metabolic Disease ; 1991 ; 14(3) ; 285-8
Watkins ; PA ; 6367 ; Phytanic acid activation in rat liver peroxisomes is catalyzed by long- chain acyl-CoA synthetase. ; J Lipid Res ; 1996 ; 37(11) ; 2288-95
Wilson ; DC ; 1998* ; Progressive neuronal degeneration of childhood (Alpers syndrome) with hepatic cirrhosis. ; European Journal of Pediatrics ; 1993 ; 152(3) ; 260-2
Winberg ; LD ; 1392 ; Mechanism of phthalate-induced inhibition of hepatic mitochondrial beta-oxidation. ; Toxicology Letters ; 1995 ; 76(1) ; 63-9
Worle ; H ; 6380 ; Progressive cerebral degeneration of childhood with liver disease (Alpers Huttenlocher disease) with cytochrome oxidase deficiency presenting with epilepsia partialis continua as the first clinical manifestation. ; Clin Neuropathol ; 1998 ; 17(2) ; 63-8
Yamamoto ; S ; 4273 ; Two novel gene mutations (Glu174-->Lys, Phe383-->Tyr) causing the "hepatic" form of carnitine palmitoyltransferase II deficiency. ; Human Genetics ; 1996 ; 98(1) ; 116-118
Yen ; T.C. ; 2640 ; Liver mitochondrial respiratory functions decline with age. ; Biochem. Biophys. Res. Commun. ; 1989 ; 165 ; 944-1003
Yen ; T.C. ; 2639* ; Age-dependent increase of mitochondrial DNA deletions together with lipid peroxides and superoxide dismutase in human liver mitochondria. ; Free Radical Biology & Medicine ; 1994 ; 16 ; 207-214